CHALLENGES IN THE AIRWAY MANAGEMENT AND MONITORING OF A PATIENT WITH DYSTROPHIC EPIDERMOLYSIS BULLOSA PRESENTING WITH SQUAMOUS CELL CARCINOMA FOREARM UNDERGOING BELOW ELBOW AMPUTATION -A CASE REPORT

Dr. BR. Bageerathi, Prof. Dr. A. Ajay kumar, Dr.R. Purushotham

Abstract


Dystrophic epidermolysis bullosa is a rare inherited disorder , caused by defect in type VII collagen leading to easy peeling of epidermis and dermis. There is widespread blistering and re- epithelisation. DEB is a pre malignant condition, predisposing to squamous cell carcinoma. We are discussing a case of DEB developing to squamous cell carcinoma in forearm planned for forearm amputation.


Keywords


Dystrophic epidermolysis bullosa, squamous cell carcinoma, subclavian vein cannulation, Difficult airway.

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References


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